产品说明
生化/生理作用
3-Hydroxyisovaleryl-L-carnitine is an endogenous metabolite that can result from impairment in the leucine catabolic pathway. 3-Hydroxyisovaleryl-L-carnitine was observed in plasma and urine of patient with isolated 3-methylcrotonyl-CoA carboxylase deficiency and is used as biomarker of biotin deficiency in humans and other metabolic disorders.
基本信息
| 经验(实验)分子式 | C12H23NO5 |
| 分子量 | 261.31 |
| Beilstein | 10549761 |
产品性质
| 等级 | analytical standard |
| 质量水平 | 100 |
| 测定 | ≥90.0% (HPLC) |
| 旋光性 | [α]/D -17.0±2.0°, c = 0.1 in H2O |
| 保质期 | limited shelf life, expiry date on the label |
| 杂质 | ≤15% water (calc. on elemental analysis) |
| application(s) | clinical testing |
| 格式 | neat |
| 储存温度 | 2-8℃ |
| SMILES string | C[N+](C)(C)C[C@H](OC(CC(C)(O)C)=O)CC([O-])=O |
安全信息
| 储存分类代码 | 13 - Non Combustible Solids |
| WGK | WGK 3 |
| 闪点(F) | Not applicable |
| 闪点(C) | Not applicable |
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